Prosci/ACADM Antibody/25-092/50 ug
商品编号:
25-092
品牌:
prosci-inc
市场价:
¥6500.00
美元价:
3900.00
产品分类:
重组抗体
公司分类:
Recombinant_antibodies
联系Q Q:
3392242852
电话号码:
4000-520-616
电子邮箱:
info@ebiomall.com
商品介绍
Specifications
SPECIES REACTIVITY: | Human |
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TESTED APPLICATIONS: | ELISA, WB |
APPLICATIONS: | ACADM antibody can be used for detection of ACADM by ELISA at 1:1562500. ACADM antibody can be used for detection of ACADM by western blot at 1 μg/mL, and HRP conjugated secondary antibody should be diluted 1:50,000 - 100,000. |
USER NOTE: | Optimal dilutions for each application to be determined by the researcher. |
POSITIVE CONTROL: | 1) 721_B Cell Lysate |
PREDICTED MOLECULAR WEIGHT: | 46 kDa |
IMMUNOGEN: | Antibody produced in rabbits immunized with a synthetic peptide corresponding a region of human ACADM. |
HOST SPECIES: | Rabbit |
Properties
PURIFICATION: | Antibody is purified by peptide affinity chromatography method. |
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PHYSICAL STATE: | Lyophilized |
BUFFER: | Antibody is lyophilized in PBS buffer with 2% sucrose. Add 50 μL of distilled water. Final antibody concentration is 1 mg/mL. |
CONCENTRATION: | 1 mg/ml |
STORAGE CONDITIONS: | For short periods of storage (days) store at 4˚C. For longer periods of storage, store ACADM antibody at -20˚C. As with any antibody avoid repeat freeze-thaw cycles. |
CLONALITY: | Polyclonal |
CONJUGATE: | Unconjugated |
Additional Info
ALTERNATE NAMES: | ACADM, ACAD1, MCAD, MCADH |
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ACCESSION NO.: | NP_000007 |
PROTEIN GI NO.: | 4557231 |
OFFICIAL SYMBOL: | ACADM |
GENE ID: | 34 |
Background
BACKGROUND: | ACADM Is the medium-chain specific (C4 to C12 straight chain) acyl-Coenzyme A dehydrogenase. The homotetramer enzyme catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. Clinical phenotypes are associated with ACADM hereditary deficiency.This gene encodes the medium-chain specific (C4 to C12 straight chain) acyl-Coenzyme A dehydrogenase. The homotetramer enzyme catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. Defects in this gene cause medium-chain acyl-CoA dehydrogenase deficiency, a disease characterized by hepatic dysfunction, fasting hypoglycemia, and encephalopathy, which can result in infantile death. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. |
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REFERENCES: | 1) Nichols, M.J., (2008) Am. J. Med. Genet. A 146A (5), 610-619. |
品牌介绍
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